Dural ectasia re-definition in Marfan syndrome
نویسندگان
چکیده
منابع مشابه
DIFFUSE ARTER IAL ECTASIA IN MARFAN SYNDROME
A 22 year old male referred with palpitation. General appearance and physical exam impressed us in that the patient has Marfan syndrome. Cardiac catheterization showed diffuse arterial ectasia. We found no previous report of this generalized diffuse ectasia.
متن کاملDural ectasia in Marfan syndrome: a case control study.
BACKGROUND AND PURPOSE Dural ectasia (DE) is one of the major criteria of Marfan syndrome (MFS). Our aim was to establish the prevalence of DE in an adult population fulfilling the Ghent criteria for MFS and to assess definitions of DE. MATERIALS AND METHODS One hundred five adults with suspected MFS were included. MR imaging at 1.5T was performed unless contraindicated; then CT was obtained....
متن کاملDural ectasia as presenting symptom of Marfan syndrome.
• Vol 10 • March 2008 194 Marfan syndrome is a genetic, dominant, systemic connective tissue disease with variable clinical features, some of which are life threatening. The prevalence is 1:10,000 live births [1]. The syndrome results from mutations in the FBN1 gene, on chromosome 15, which encodes for the fibrillin 1 protein. Fibrillin is an important compound in the extracellular matrix and t...
متن کاملPrevalence of Dural Ectasia in Loeys-Dietz Syndrome: Comparison with Marfan Syndrome and Normal Controls
BACKGROUND AND PURPOSE Dural ectasia is well recognized in Marfan syndrome (MFS) as one of the major diagnostic criteria, but the exact prevalence of dural ectasia is still unknown in Loeys-Dietz syndrome (LDS), which is a recently discovered connective tissue disease. In this study, we evaluated the prevalence of dural ectasia in LDS according by using qualitative and quantitative methods and ...
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Marfan syndrome (MFS) is a genetic disorder of connective tissue, characterized by variable clinical features and multisystem complications. The anesthetic management during delivery is debated. Regional anesthesia has been used with success during cesarean delivery, but in some MFS patients there is a probability of erratic and inadequate spread of intrathecal local anesthetics as a result of ...
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ژورنال
عنوان ژورنال: Archives of Cardiovascular Diseases Supplements
سال: 2019
ISSN: 1878-6480
DOI: 10.1016/j.acvdsp.2018.10.124